Journal of Pediatric Neurology 2009; 07(04): 423-426
DOI: 10.3233/JPN-2009-0329
Case Report
Georg Thieme Verlag KG Stuttgart – New York

Congenital rubella syndrome presenting at birth with blueberry muffin rash and communicating hydrocephalus

Sriparna Basu
a   Neonatal Unit, Department of Pediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India
,
Aditya Kumar Gupta
a   Neonatal Unit, Department of Pediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India
,
Ayan Kumar
a   Neonatal Unit, Department of Pediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India
,
Poonam Singh
a   Neonatal Unit, Department of Pediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India
,
Ashok Kumar
a   Neonatal Unit, Department of Pediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India
› Author Affiliations

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Further Information

Publication History

29 October 2008

25 January 2009

Publication Date:
30 July 2015 (online)

Abstract

We report a preterm, small-for-gestational age, very low birth weight male neonate presenting at birth with generalized reddish blue papulonodular lesions (including palms and soles), anemia, thrombocytopenia, hepatosplenomegaly, interstitial pneumonitis, sensorineural deafness, atrial septal defect, and communicating hydrocephalus. A diagnosis of blueberry muffin rash in a child with congenital rubella syndrome and communicating hydrocephalus was made based on clinical and laboratory findings. The rash disappeared by 10th day of life.