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Semin intervent Radiol 2022; 39(03): 261-270
DOI: 10.1055/s-0042-1751260
Review Article

Pulmonary Arteriovenous Malformations: What the Interventional Radiologist Should Know

Claire S. Kaufman
1   Dotter Department of Interventional Radiology, Pacific Northwest HHT Center of Excellence, Oregon Health & Sciences University, Portland, Oregon
,
Jamie McDonald
2   Department of Pathology, University of Utah, Salt Lake City, Utah
,
Heather Balch
3   HHT Center of Excellence, Department of Internal Medicine, University of Utah, Salt Lake City, Utah
,
Kevin Whitehead
4   HHT Center of Excellence, Division of Cardiovascular Medicine, University of Utah, Salt Lake City, Utah
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Abstract

Pulmonary arteriovenous malformations (PAVMs) are abnormal connections between the pulmonary artery and pulmonary vein bypassing the normal capillary bed causing a right-to-left shunt. The majority (80–90%) of PAVMs are associated with hereditary hemorrhagic telangiectasia (HHT). PAVMs may be asymptomatic or present with symptoms of hypoxia, shortness of breath, migraines, sequelae of paradoxical embolization, or rupture. Transcatheter embolization has become the standard of care. This article will review the clinical presentation, workup, genetics, imaging findings, embolization, complications, and follow-up for patients with PAVMs.

Keywords

hereditary hemorrhagic telangiectasia - pulmonary arteriovenous malformation - embolization - interventional radiology


Publikationsverlauf

Artikel online veröffentlicht:
31. August 2022

© 2022. Thieme. All rights reserved.

Thieme Medical Publishers, Inc.
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