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J Neurol Surg A Cent Eur Neurosurg 2022; 83(03): 294-297
DOI: 10.1055/s-0041-1722969
Case Report

Epithelioid Hemangioendothelioma in the Area of the Neurovascular Bundle of the Upper Arm Mimicking a Schwannoma of the Ulnar Nerve

Christian Scheller
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Stefan Rampp
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Julian Prell
2   Department of Neurosurgery, University Hospital Halle (Saale), Halle (Saale), Germany
,
Christian Strauss
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Endres John
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Ukkat Jörg
3   Department of General Surgery, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
,
Linda Diessel
4   Department of Pathology, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
,
Silvio Brandt
5   Department of Neuroradiology, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
,
Tobias Müller
6   Department of Neurology, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
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Abstract

Epithelioid hemangioendothelioma (EH) is a rare vascular malignant sarcoma. To date, there are only two published case reports of EH mimicking nerve sheath tumors of a peripheral nerve. A 41-year-old woman presented with a painful node on the inside of the upper arm and motor deficits of the ulnar nerve. Magnetic resonance imaging (MRI) follow-up and neurosonography revealed a slowly progressive, contrast-enhancing tumor in the area of the neurovascular bundle. A schwannoma of the ulnar nerve was suspected. At surgery, the tumor was adherent to the brachial artery, but not to nerves. Pathology revealed an EH. EH may mimic a nerve sheath tumor and should be taken into consideration, especially because of its potential for metastasis and fatal progression.

Keywords

epithelioid hemangioendothelioma - peripheral nerve - vascular neoplasm

Patient Consent

The patient has consented to the submission of the case report for submission to the journal.




Publication History

Received: 23 June 2020

Accepted: 22 September 2020

Article published online:
12 April 2021

© 2021. Thieme. All rights reserved.

Georg Thieme Verlag KG
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