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Eur J Pediatr Surg 2020; 30(03): 279-286
DOI: 10.1055/s-0040-1713597
Review Article
Georg Thieme Verlag KG Stuttgart · New York

Health-Related Quality of Life and Psychosocial Morbidity in Anorectal Malformation and Hirschsprung's Disease

Xiaoyan Feng
1   Department of Pediatric Surgery, Leipzig University, Leipzig, Sachsen, Germany
,
Martin Lacher
1   Department of Pediatric Surgery, Leipzig University, Leipzig, Sachsen, Germany
,
Julia Quitmann
2   Department of Medical Psychology, University Medical Center, Hamburg, Eppendorf, Germany
,
Stefanie Witt 
2   Department of Medical Psychology, University Medical Center, Hamburg, Eppendorf, Germany
,
Marieke J. Witvliet
3   Department of Pediatric Surgery, UMC Utrecht, Utrecht, The Netherlands
,
Steffi Mayer
1   Department of Pediatric Surgery, Leipzig University, Leipzig, Sachsen, Germany
› Author Affiliations
Further Information

Publication History

15 May 2020

25 May 2020

Publication Date:
26 June 2020 (online)

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Abstract

Anorectal malformation (ARM) and Hirschsprung's disease (HD) are the most common congenital colorectal anomalies. Despite advances in surgical techniques and improvements in postoperative clinical care, short- and long-term physical and psychosocial morbidity of these patients remains high. This review outlines the current literature on the physical and psychosocial aspects of health-related quality of life (HrQoL) and its confounders in patients with ARM/HD. Moreover, important coping strategies are summarized to further improve HrQoL of ARM/HD patients and their families.

Keywords

anorectal malformation - Hirschsprung's disease - bowel function - psychosocial morbidity - health-related quality of life
 

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