Subscribe to RSS
Please copy the URL and add it into your RSS Feed Reader.
https://www.thieme-connect.de/rss/thieme/en/10.1055-s-00034925.xml
Download PDF
Hamostaseologie 1987; 07(01): 24-28
DOI: 10.1055/s-0038-1660368
DOI: 10.1055/s-0038-1660368
Originalarbeit
Der kongenitale Faktor-V-Mangel
Authors
Further Information
Publication History
Publication Date:
25 June 2018 (online)
-
LITERATUR
- 1 Alexander B, Goldstein R. Parahemophilia in three siblings (Owren’s disease) with studies on certain plasma components affecting prothrombin conversion. Am J Med 1952; 13: 255-72.
- 2 Almagro D, Corral J F, Cruz A. Parahemofilia (deficit congénito de factor V). Rev Invest Clin 1974; 26: 175-9.
- 3 Ambriz-Fernandéz R, Villasenor A, Reyna M P, Pizzuto J. et al. Coagulation factors V and VII combined congenital deficiency. Arch Invest Med (Mex) 1985; 16: 59-70.
- 4 Åstrup T. In: Advances in Enzymology. Bd. 10. Nord F F. (ed). New York: Interscience Publishers; 1950
- 5 Badurowa A, Galazka Z, Sciborski R. Oral surgery in a patient with congenital factor V deficiency. Wiad Lek 1983; 36: 1797-800.
- 6 Barthels M, Poliwoda H. Gerinnungsanalysen. Stuttgart: Thieme; 1987
- 7 Baugh C W. Parahemophilia (congenital factor V deficiency). Canad Med Assoc J 1965; 92: 979-81.
- 8 Borchgrevink C F, Owren P A. Surgery in a patient with factor V deficiency. Acta Med Scand 1961; 170: 743-6.
- 9 Borchgrevink C F, Owren P A. The hemostatic effect of normal platelets in hemophilia and factor V deficiency. Acta med Scand 1961b 170: 375-83.
- 10 Breederveld K, Giddings J G, Ten Cate J W, Bloom A L. The localization of factor V within normal human platelets and the demonstration of a platelet factor V antigen in congenital factor V deficiency. Br J Haematol 1975; 29: 405-12.
- 11 Brennan M J, Monto R W, Shafer H C. Hemorrhagic diathesis due to Ac-globulin deficiency. Am J Clin Path 1952; 22: 150.
- 12 Brink A J, Kingsley C S. A familial disorder of blood coagulation due to deficiency of the labile factor. Q J Med 1952; 21: 19-31.
- 13 Brink S. Inherited factor V deficiency (parahemophilia): a case report. S Afr Med J 1974; 48: 537-9.
- 14 Brown J W, Smith W M, Howse R N. Surgical management in hemophilia and hemophiloid diseases. Ann Surg 1959; 149: 721.
- 15 Butto M, Grizzo G. La Paraemofilia. Friuli med 1967; 22: 911-32.
- 16 Cantarutti F, Sparta D. Deficit congenito di proaccelerina (paraemofilia di Owren). Porpora nodulare cutanea e grave emorragia endoculare. Acta paediat lat 1965; 18: 175.
- 17 Centurelli G. La malattia di Owren o parahemophilia. Rass Fisiopat Clin ter 1963; 35: 452.
- 18 Cetnarowicz H, Latallo Z, Piechocka T, Zaluska W. Przypadek wrodzonego nièdoborn czynnika V. Pol Arch Med Wewnet 1962; 32: 757-9.
- 19 Chediak J. Successful management of bleeding in a patient with factor V inhibitor by platelet transfusions. Blood 1980; 56: 835-41.
- 20 Coelho E, Verrastro T, Jamra M. Parahemofilia. A presentacao de caso de deficienca de factor V. Rev Hosp Clin 1957; 12: 216.
- 21 Das K C, Metha S. Congenital factor V deficiency (parahemofilia) in two siblings. J Indian Med Assoc 1968; 51: 403-6.
- 22 Deutsch E. Über die Thrombokinasebildung und das Verhalten von Thrombozytenfaktor 1 bei Hypoproakzelerinämie (Parahämophilie). Wien Z Inn Med 1955; 36: 355-7.
- 23 De Vries A, Matoth Y, Shamir Z. Familial congenital labile factor deficiency with syndactilism. Acta Haemat 1951; 05: 129.
- 24 Faeth W H. A hemorrhagic diathesis due to proaccelerin deficiency (congenital parahemophilia). A case report. Conn med J 1953; 17: 664.
- 25 Fajardo L F, Silvert D. Pregnancy and Ac-globulin deficiency. Am J Obst Gynec 1957; 74: 909.
- 26 Llamazares Fernandez, Rodriguez J, Lòpez AHernandez, Zuazu JNagore, Fort J MLopez Baragas, Sueiras AFechtenburg. Recurrent hemoperitoneum: congenital coagulopathy and endometriosis. Med Clin 1983; 08: 455-6.
- 27 Field J B, Ware A. Studies in parahemophilia. J Clin Invest 1954; 33: 932.
- 28 Fijnvandraat L J, van Wermaskerkern R K. A family with factor V deficiency (parahemophilia). Neth J Med 1976; 19: 135-40.
- 29 Fischer R R, Pereira V W, Pereira D V, Roisenberg J. Inherited factor V deficiency. Study of a Brazilian family. Hum Hered 1984; 226-30.
- 30 Frank E, Bilhan N, Eckren H. Die Parahämophilie (Owren) eine neue Form der hämorrhagischen Diathese. Acta haemat 1950; 03: 70-90.
- 31 Friedmann J A, Quick A J, Higgins F, Hussey C V, Hickley M. Hereditary labile factor (factor V) deficiency. J Am Med Ass 1961; 175: 370-4.
- 32 Galazka Z. Surgical procedures in a patient with congenital deficiency of factor V (proaccelerin). Ginecol Pol 1984; 55: 225-8.
- 33 Garcia Ade Larre Borges, Barsumian Mde Kurdian. Parahemofilia: deficiencia aislada de proacelerina (factor V). Ann Fac Med Montevideo 1960; 45: 235.
- 34 Girolami A, Scarpa R, Cadrobbi P. Haemorrhagic varicella in parahemophilia. Blut 1972; 25: 293-301.
- 35 Girolami A, Venturelli R, Righini F, Scarpa R. Parahemophilia. A case report. Acta Haemat 1971; 46: 242-53.
- 36 Gobbi F, Ascari E, Barbieri U. Deficit congenito di proaccelerina (parahemofilia di Owren). Minerva med 1960; 51: 78-87.
- 37 Hauser F. Idiopathische Hypoprothrombinämie versus Mangel an Faktor V. Ann Paediatrica 1950; 174: 19.
- 38 Heni F, Krauss J. Angeborener Faktor-VMangel (Owren’sche Krankheit). Klin Wschr 1954; 32: 633.
- 39 Hjort P F, Rapaport S J, Owren P A. Evidence that platelet accelerator (platelet factor 1) is absorbed plasma proaccelerine. Blood 1955; 10: 1139-50.
- 40 Hörder M H. Isolierter Faktor-V-Mangel bedingt durch einen spezifischen Hemmkörper. Acta Haemat 1955; 13: 235.
- 41 Hörder M H, Hiemeyer V. Kongenitaler Faktor-V-Mangel. Med Klinik 1963; 58: 2042-7.
- 42 Ikkala E, Myllylä G, Nevanlinna H R. Rare congenital coagulation defects in Finnland. Scand J Haematol 1971; 08: 210-5.
- 43 Iversen T, Bastrup PMadsen. Congenital familial deficiency of factor V (parahaemophilia) combined with deficiency of antihaemophilic globulin. Br J Haemat 1956; 02: 265.
- 44 Kagami M, Morita H. Parahaemophilia. Acta Haemat 1966; 35: 102-12.
- 45 Kingsley C S. Familial factor V deficiency: the pattern of heredity. Quart J Med 1954; 23: 323.
- 46 Kleimans M, Barraza O R, Kordich L, Zdrojewsky D. Deficit congenito de factor V. Sangre 1966; 11: 379-82.
- 47 Klinowska W, Morawska Z, Krcemién K. Familial proaccelerine (factor V) deficiency. Pol Tyg Lek 1973; 28: 1919-22.
- 48 Kwa S P, Chen Y F. Congenital factor V deficiency report on a case. Singapore Med J 1965; 06: 184-91.
- 49 Langer R. Management of labor in a patient with factor V deficiency. Isr J Med Sci 1982; 18: 701-3.
- 50 Larrieu M J, Caen J, Grenet P, Cayla J, Bernard J. Hypoaccélérinémia congénitale (parahémophilie d’ Owren). Sang 1956; 27: 117.
- 51 Lewis J H, Ferguson J H. Hypoproaccelerinemia. Blood 1955; 10: 351.
- 52 Löpez V, Pflugshaupt R, Wirthner W, Bütler R. Hereditärer Faktor-V-Mangel (Parahämophilie) in einer Schweizer Familie. Schweiz Med. Wochenschr 1969; 99: 1354-6.
- 53 Löpez-Botet E, Vilar E. Dos casos de parahemofilia por carenzia de factor V y VII de Owren. Rev Clin Espan 1955; 58: 220.
- 54 Losay J. Surgical correction of coarctation of the aorta and ventricular septum defect in an infant with inherited factor V deficiency (letter). Pediatr Cardiol 1983; 04: 169-70.
- 55 Mammen E F. Congenital coagulation disorders. Semin Thrombos Haemostas 1983; 09: 17-8.
- 56 Mandelli F, Gandolfo G M, Isacchi G, Mariani G, Miracelli A. La malattia emorragica da carenza di fattore V (paraemofilia). Rec Progr Med 1971; 51: 71-98.
- 57 Marx R. Konstitutionelle Pseudohypoprothrombinämien. Ärztl Forsch 1950; 04: 567-76.
- 58 Mazzucconi M G. Inhibitor to factor V in severe factor V congenital deficiency. Nouv Rev Fr Hematol 1985; 27: 303-5.
- 59 Melliger E J, Duckert F. Major surgery in a subject with factor V deficiency. Thrombos Diathes haemorrh 1971; 25: 438-446.
- 60 Miletich J P, Majerus D W, Majerus P W. Patients with congenital factor V deficiency have decreased factor Xa binding sites on their platelets. J Clin Invest 1978; 62: 824-31.
- 61 Miller S P, Siggerud J, Stefanski T. Coagulation dynamics in factor V deficiency: a family study with a note on the occurence of thrombophlebitis. Thrombos Diathes haemorrh 1965; 13: 500-15.
- 62 Mitterstieler G, Müller W, Geir W. Congenital factor V deficiency. A family study. Scand J Hematol 1978; 21: 9-13.
- 63 Morita H, Kagami M, Miyoshi Y. On a case of Owren’s disease. Clin Hematology 1960; 01: 55.
- 64 Nielsen J D. Parahemophilia-factor V deficiency. Ugeskr laeger 1980; 142: 582-3.
- 65 O’Brien J R. Factor V in blood coagulation in vitro and a report of a case of factor V deficiency. Br J Haemat 1958; 04: 210.
- 66 Oeri J, Matter M, Isenschmid H, Hauser F, Koller F. Angeborener Mangel an Faktor V (Parahämophilie) verbunden mit echter Hämophilie A bei zwei Brüdern. Bibi paediat 1954; 58: 575.
- 67 Outeirino H J, Sânchez JFayos, Paniagua G, Hernando LAvenado, Aguirre MJaca. Parahemophilia defecto congenito de factor V. Rev Clin Esp 1966; 101: 56-8.
- 68 Owen Jr C A, Cooper T. Parahemophilia. Arch Intern Med 1955; 95: 194-201.
- 69 Owren P A. Parahaemophilia, haemorrhagic diathesis due to absence of a previously unknown clotting factor. Lancet 1947; 01: 446-8.
- 70 Owren P A. Prothrombin and accessory factors. Am J Med 1953; 14: 201.
- 71 Pecikyan R. Parahémophilie (Owren) avec hémarthrose chez deux soeurs. New Istanbul Contr Clin Sci 1955; 03: 199.
- 72 Phillips L L, Little W A. Factor V deficiency in obstetrics. Obstet Gynec 1962; 19: 507-12.
- 73 Quick A J. On the constitution of prothrombin. Am J Physiol 1943; 140: 212-20.
- 74 Redner B, Scalettar H, Weiner M. Parahemophilia (Owren’s Disease). Pediatrics 1953; 12: 5.
- 75 Reich E N, Hoffman G C, de Wolfe V G, Van Ordstrand H S. Recurrent thrombophlebitis and pulmonary emboli in congenital factor V deficiency. Chest 1976; 69: 113-4.
- 76 Retief F P. Owren se siekte (Kongenitale Factor V Tekort, Parahemophilie) by twee Kleurlingsusters. S Afr Med J 1964; 38: 544-7.
- 77 Rotoli B, Formisano S. Factor V deficiency (parahemophilia). Study of a family. Curr Top Microbiol Immunol 1975; 70: 823-42.
- 78 Rush B, Ellis H. The treatment of patients with factor V deficiency. Thrombos Diathes haemorrh 1965; 14: 74-82.
- 79 Sacks M S, Raccuglia G. Hereditary deficiency of proaccelerin (parahemophilia). J Lab Clin Med 1955; 46: 98.
- 80 Sailer S, Hinrichs R. Isolierter Kongenitaler Faktor-V-Mangel als Ursache einer hämorrhagischen Diathese. Wien Inn Med 1959; 40: 10.
- 81 Saint PPaul, Chassaigne M. Déficit majeur en proaccélérine (Facteur V) d’origine congénitale. »Maladie d’Owren«. Gaz Méd France 1966; 73: 707.
- 82 Santangelo G, Caponetti R, Buda D. La paraemofilia nell eta neonatale. Haemat Archivio 1966; 51: 705.
- 83 Satake K, Takazawa T, Hynnya H, Yahata K, Watanuki M. On a case of slight parahemophilia (idiopathic factor V deficiency). Naika 1964; 14: 530-6.
- 84 Schulman J, Smith C H. Coagulation disorders in infancy and childhood. Adv Paediatr 1957; 09: 231.
- 85 Seeler R A. Parahemophilia. Factor V deficiency. Med Clin North Am 1972; 56: 119-25.
- 86 Seibert R H, Marjolius A, Ratnoff O D. Observations on hemophilia, parahemophilia and coexistent hemophilia and parahemophilia. J Lab Clin Med 1958; 52: 449.
- 87 Shanahan F, Aburajab A, Goodacre R, Blajchman M A. Factor V deficiency and its reversal with gluten restriction in a patient with celiac disease. Arch Intern Med 1983; 143: 2009-10.
- 88 Siegert E, Quietzsch J. Ein seltener Fall von Hämaturie: Parahämophilie. Kinderärztl Prax 1984; 52: 344-6.
- 89 Singh G, Das K C. Haemophiloid disorder. Indian J Med Sci 1968; 22: 623-6.
- 90 Soulier J P, Proü OWartelle, Weilland C, Ménaché D. Deficient congenital en proaccelerine (facteur V) quelques données nouvelles. Thrombos Diathes Haemorrh 1958; 02: 250.
- 91 Sparta D, Bonifaci E. Su di un raro caso di deficit congenito di proaccelerina associato a morbo di Werlhof. Acta Paediat Lat 1964; 17: 134.
- 92 Stohlmann F, Harrington W J, Moloney W C. Parahemophilia (Owren’s Disease). Report of a case in a women with studies on other members of her family. J Lab Clin Med 1951; 38: 842-5.
- 93 Tango M, Ujiie A, Ishikawa N, Yasukonchi T. Familial congenital factor V deficiency (parahemophilia). J Jap Soc Intern Med 1965; 54: 816-20.
- 94 Terheggen H G. Faktor-V-Mangel bei einem 8 Monate alten Mädchen. Monatsschr Kinderheilkd 1971; 119: 627-32.
- 95 Tracy P B, Eide L L, Bowie E J W, Mann K G. Radioimmunassay of factor V in human plasma and platelets. Blood 1982; 60: 59-63.
- 96 Tracy P B, Giles A R, Mann K G, Eidè L L, Hoogendoorn H, Rivard G E. Faktor V (Quebec) a bleeding diathesis associated with a qualitative platelet factor V deficiency. J Clin Invest 1984; 74: 1221-8.
- 97 Vickars L M. The response of an acquired factor V inhibitor to activated factor IX concentrate. Transfusion 1985; 25: 51-3.
- 98 Ware A G, Guest M, Seegers W H. Plasma accelaerator factor and purified prothrombin activation. Science 1947; 106: 41.
- 99 Webster W P, Roberts H R, Peuck G D. Hemostasis in factor V deficiency. Am J Med Sci 1964; 248: 194-202.
- 100 Whitelaw A, Haines M E, Bolsover W, Harris E. Factor V deficiency and antenatal intraventricular hemorrhage. Arch Dis Child 1984; 59: 997-9.
- 101 Winckelmann G, Walther C. Zur Substitutionsbehandlung beim kongenitalen Faktor-V-Mangel. Blut 1968; 16: 345-50.
- 102 Yoshioka A, Fugimura Y. Kitawaki, et al. A case of congenital factor V deficiency. Report of a case and review of 28 reported cases in Japan. Jpn J Clin Hematol 1975; 16: 953-62.