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Klin Monbl Augenheilkd 2024; 241(04): 529-532
DOI: 10.1055/a-2211-9248
Der interessante Fall

A Case of Congenital Stationary Night Blindness in a Healthy Female Infant: Emphasis on Electroretinography

Eine Fallvorstellung über kongenitale stationäre Nachtblindheit bei einem gesunden Mädchen: mit Elektroretinografie als Schwerpunkt
Dmitri Artemiev
1   Department of Ophthalmology, Cantonal Hospital St. Gallen, St. Gallen, Switzerland
,
Margarita G. Todorova
1   Department of Ophthalmology, Cantonal Hospital St. Gallen, St. Gallen, Switzerland
2   Department of Ophthalmology, University Hospital Basel, Basel, Switzerland
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Background

Congenital stationary night blindness (CSNB) is a rare nonprogressive retinal disorder characterised by congenitally impaired night vision and subnormal visual acuity. Important associated clinical hallmarks in CSNB are myopic refractive error, astigmatism, strabismus, and paradoxical pupillary responses. In some cases, nystagmus may also be present [1], [2].



Publication History

Received: 05 October 2023

Accepted: 13 November 2023

Article published online:
23 April 2024

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