CC BY-NC-ND 4.0 · Asian J Neurosurg 2017; 12(02): 241-243
DOI: 10.4103/1793-5482.144169
CASE REPORT

A common case with an unusual association: Chiari I malformation with holocord syrinx

Sumit Bansal
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi
,
Sachin Borkar
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi
,
Ashok Mahapatra
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi
› Author Affiliations

Authors are presenting a common case of Chiari malformation but with a very unusual associated finding, holocord syringomyelia, which responded to posterior fossa decompression. An 11-year-old male patient presented with progressive left hemiparesis and numbness on left half of the body for 4 years. Magnetic resonance imaging of the spine revealed peg-shaped herniation of tonsils 8 mm below the foramen magnum and holocord syringomyelia. No focal intraspinal mass was seen. Chiari I malformation with holocord syrinx was diagnosed. The patient underwent posterior fossa decompression with subpial resection of both tonsils with augmentation duraplasty. Post-operatively, patient improved clinically as well as radiologically.



Publication History

Article published online:
20 September 2022

© 2017. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

Thieme Medical and Scientific Publishers Pvt. Ltd.
A-12, 2nd Floor, Sector 2, Noida-201301 UP, India