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CC BY-NC-ND 4.0 · Journal of Fetal Medicine
DOI: 10.1055/s-0044-1780492
Case Report

Prenatal Diagnosis of Renal Rhabdoid Tumor: A Rare Malignant Neoplasm

Vidhika Berwal
1   Division of Fetal Medicine & Perinatology, Amrita Institute of Medical Sciences & Research Centre, Kochi, Kerala, India
,
Vivek Krishnan 
1   Division of Fetal Medicine & Perinatology, Amrita Institute of Medical Sciences & Research Centre, Kochi, Kerala, India
,
Malini Eapen
2   Department of Pathology, Amrita Institute of Medical Sciences & Research Centre, Kochi, Kerala, India
,
Vidya Chandraprabha
2   Department of Pathology, Amrita Institute of Medical Sciences & Research Centre, Kochi, Kerala, India
,
Rinshi Abid Elayedatt 
1   Division of Fetal Medicine & Perinatology, Amrita Institute of Medical Sciences & Research Centre, Kochi, Kerala, India
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Abstract

Rhabdoid tumors of the kidney are highly lethal malignancies of infancy. We report the prenatal detection of this renal tumor in a fetus in the third trimester of pregnancy. Ultrasonologically, the tumor appeared as a large mass in the left renal area associated with severe polyhydramnios. Though the sonographic features alone did not allow distinction from a benign lesion, tumor extension into the subcutaneous plane favored the possibility of a malignant renal tumor and this was confirmed postnatally on histopathology.

Keywords

rhabdoid tumor - rare renal neoplasm - malignant renal tumor - prenatal diagnosis - prenatal ultrasound

Informed Consent

Written informed consent was obtained from the patients for participation and publication of this study.


Ethical Approval

This was in accordance with the ethical standards of the institutional and national research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards.


Authors' Contributions

All authors contributed to the study's conception and design. All authors have read and approved the final manuscript.




Publication History

Article published online:
10 April 2024

© 2024. Society of Fetal Medicine. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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