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Eur J Pediatr Surg 2014; 24(06): 467-473
DOI: 10.1055/s-0034-1396424
Review Article
Georg Thieme Verlag KG Stuttgart · New York

A Review on Surgical Techniques and Organ Sparing Procedures in Bladder/Prostate Rhabdomyosarcoma

Leszek Komasara
1   Department of Pediatric Surgery and Urology for Children and Adolescents, Medical University in Gdansk, Pomerania, Poland
*   The authors, Dr. Leszek Komasara and Dr. Andrzej Golebiewski, contributed equally to this review.
,
Andrzej Gołębiewski
1   Department of Pediatric Surgery and Urology for Children and Adolescents, Medical University in Gdansk, Pomerania, Poland
*   The authors, Dr. Leszek Komasara and Dr. Andrzej Golebiewski, contributed equally to this review.
,
Stefan Anzelewicz
1   Department of Pediatric Surgery and Urology for Children and Adolescents, Medical University in Gdansk, Pomerania, Poland
,
Piotr Czauderna
1   Department of Pediatric Surgery and Urology for Children and Adolescents, Medical University in Gdansk, Pomerania, Poland
› Institutsangaben
Weitere Informationen

Publikationsverlauf

31. Oktober 2014

04. November 2014

Publikationsdatum:
08. Dezember 2014 (online)

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Abstract

The treatment outcomes in children with bladder/prostate rhabdomyosarcoma (B/P RMS) have considerably improved in the past few decades. Current protocols incorporate chemotherapy, radiotherapy, and surgery (radical or organ sparing). Using this multimodal and multidisciplinary approach, the cure rates for nonmetastatic RMS have gradually increased from 25% in the 1970s, and 70% in the 1990s, to over 80% in the 2000s. Surgery plays a role not only in the diagnosis and management of all stages of B/P RMS, but also in the urinary reconstruction and long-term follow-up. Furthermore, the tendency to avoid mutilating surgery and to preserve functional genitourinary tract has been noticeable. Authors describe the current status and future surgical treatment approaches and possibilities for patients with B/P RMS and how reconstructive urologic surgery in B/P RMS continues to evolve.

Keywords

rhabdomyosarcoma - genitourinary - pediatric - surgery - organ sparing
 

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