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CC BY-NC-ND 4.0 · AJP Rep 2023; 13(03): e40-e43
DOI: 10.1055/a-2107-0651
Case Report

Unilateral Lung Agenesis: A Case Series and Review of Literature

Jennifer Weber
1   Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin
,
Sunil Kumar Sati
2   Division of Neonatology, Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin
,
Vijender Rao Karody
2   Division of Neonatology, Department of Pediatrics, Medical College of Wisconsin, Milwaukee, Wisconsin
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Abstract

Unilateral lung agenesis is a rare congenital abnormality that typically presents with respiratory distress after birth. Prognostic factors include the side of the lung affected along with the presence or absence of other congenital abnormalities. Prenatal imaging can make the diagnosis that can assist the healthcare team in preparing to care for the neonate, as well as set expectations for the family. In this case series, we describe three cases of unilateral lung agenesis, two infants with right lung agenesis, and one with the left. We describe their presentation, provide a brief clinical course, and discuss outcomes.

Keywords

unilateral lung agenesis - congenital abnormality - neonate - respiratory distress after birth


Publication History

Received: 18 April 2023

Accepted: 23 May 2023

Accepted Manuscript online:
07 June 2023

Article published online:
14 July 2023

© 2023. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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