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DOI: 10.1055/s-2002-23636
© Georg Thieme Verlag Stuttgart · New York
Endosonography-Guided Celiac Plexus Neurolysis in the Treatment of Pain Secondary to Acute Intermittent Porphyria
Publication History
6 June 2001
9 October 2001
Publication Date:
03 April 2002 (online)
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Acute intermittent porphyria is a metabolic error transmitted as an autosomal dominant disorder with incomplete penetrance. Its clinical picture includes intermittent abdominal pain, nausea, vomiting, and diarrhea, with or without neurological changes. We report the case of a young woman whose pain attacks were controlled with high-dose opiates, in whom we decided to perform endosonography-guided celiac plexus neurolysis (EUS-CPN). This is the first reported attempt with this new treatment option. There was significant clinical and nutritional improvement after treatment.
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A. P. Ferrari, M.D.
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