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Journal of Pediatric Neuroradiology 2016; 05(04): 256-262
DOI: 10.1055/s-0036-1597688
Case Report
Georg Thieme Verlag KG Stuttgart • New York

Spontaneous Occlusion of a Vein of Galen Malformation: A Case Report and Proposed Mechanism

Christopher Storey
1   Department of Neurosurgery, Louisiana State University Health Sciences Center Shreveport, Shreveport, Louisiana, United States
,
Christina Notarianni
1   Department of Neurosurgery, Louisiana State University Health Sciences Center Shreveport, Shreveport, Louisiana, United States
,
Anil Nanda
1   Department of Neurosurgery, Louisiana State University Health Sciences Center Shreveport, Shreveport, Louisiana, United States
,
Hugo Cuellar-Saenz
1   Department of Neurosurgery, Louisiana State University Health Sciences Center Shreveport, Shreveport, Louisiana, United States
› Author Affiliations
Further Information

Publication History

09 August 2016

01 October 2016

Publication Date:
26 December 2016 (online)

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Abstract

A vein of Galen malformation (VGM) is a rare condition of the pediatric population. Our patient was diagnosed with VGM on intrauterine ultrasound. At birth, she was noted to have multiple congenital heart defects but no signs of congestive heart failure, and intervention was delayed. Our patient presented at 4 months of age with worsening hydrocephalus due to the enlargement of the VGM. A ventricular peritoneal shunt was placed. At 26 months of age, our patient was taken for embolization of the VGM. Cerebral angiography showed no VGM. We present that changes in hemodynamics after shunt placement lead to the thrombosis of the VGM.

Keywords

hydrocephalus - pediatric - spontaneous occlusion - vein of Galen malformation - ventricular peritoneal shunt
 

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