Isolated Horner Syndrome and Orbital Hemangioma

Background

Horner syndrome results from an interruption of the three-neuron oculosympathetic pathway. The classic presentation of Horner syndrome is a combination of ipsilateral miosis, mild upper eyelid ptosis, and facial anhydrosis. In children, the presence of Horner syndrome in the absence of obvious trauma (neonatal or perinatal) is worrisome as neuroblastoma is a classic albeit rare cause of sympathetic dysfunction (2 % of cases) [1]. The recommended work-up of a child with Horner syndrome is general physical examination, palpation of the neck, axilla and abdomen, MRI of the head, neck, chest and abdomen in addition to urine studies for catecholamines (homovanillic acid [HVA] and vanillylmandelic acid [VMA]) [1]. The other causes of Horner syndrome are numerous, but an isolated Horner syndrome is not suggestive of an orbital lesion [1]. We report an isolated Horner syndrome in a 5-month-old boy which resulted from a presumed orbital hemangioma.

• References

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