Thorac Cardiovasc Surg 2010; 58(8): 492-493
DOI: 10.1055/s-0030-1250158
Special Report

© Georg Thieme Verlag KG Stuttgart · New York

Early Surgical Management of Chylothorax Complicated by Gorham's Disease

Y. K. Seok1 , S. Cho1 , E. Lee1
  • 1Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital, Daegu, Republic of Korea
Further Information

Publication History

received May 23, 2010

Publication Date:
25 November 2010 (online)

Abstract

Gorham's disease is a rare disorder and its etiology remains unknown. It is characterized by the proliferation of vascular structures in bone, and results in progressive osteolysis. Chylothorax is a severe complication of Gorham's disease with a mortality of 50 %. We report a 14-year-old boy with Gorham's disease complicated by chylothorax who underwent early surgical management followed by radiotherapy.

References

  • 1 Gorham L W, Stout A P. Massive osteolysis (acute spontaneous absorption of bone, phantom bone, disappearing bone).  J Bone Joint Surg [Am]. 1955;  37 985-1004
  • 2 Patel D V. Gorham's disease or massive osteolysis.  Clin Med Res. 2005;  3 65-74
  • 3 Tie M L, Poland G A, Rosenow E C. Chylothorax in Gorham's syndrome. A common complication of a rare disease.  Chest. 1994;  105 208-213
  • 4 Pfleger A, Schwinger W, Maier A et al. Gorham-Stout syndrome in a male adolescent – case report and review of the literature.  J Pediatr Hematol Oncol. 2006;  28 231-233
  • 5 Avelar R L, Martins V B, Antunes A A et al. Use of zoledronic acid in the treatment of Gorham's disease.  Int J Pediatr Otorhinolaryngol. 2010;  74 319-322

Dr. Eungbae Lee, MD, PhD

Department of Thoracic and Cardiovascular Surgery
Kyungpook National University Hospital

200 Dongduk-ro Jung-gu

Daegu 700-721

Republic of Korea

Phone: +82 5 34 20 56 65

Fax: +82 5 34 26 47 65

Email: bay@knu.ac.kr