Thorac Cardiovasc Surg 2010; 58(6): 369-372
DOI: 10.1055/s-0029-1240834
Case Reports

© Georg Thieme Verlag KG Stuttgart · New York

Interruption of the Inferior Vena Cava and Azygos Continuation in a Child with Partial Atrioventricular Septal Defect

B. Erkut1 , A. Ates2 , S. Arslan3 , M. A. Kaygin1 , O. Dag1 , F. Alper4
  • 1Cardiovascular Surgery, Erzurum Training and Research Hospital, Erzurum, Turkey
  • 2Cardiovascular Surgery, Atatürk University Medical Faculty, Erzurum, Turkey
  • 3Cardiology, Atatürk University Medical Faculty, Erzurum, Turkey
  • 4Radiology, Atatürk University Medical Faculty, Erzurum, Turkey
Further Information

Publication History

received September 4, 2009

Publication Date:
07 September 2010 (online)

Abstract

Congenital pathologies of the inferior vena cava are uncommon. Isolated congenital interruption of the inferior vena cava with azygos vein continuation could be considered part of the group of venous return anomalies. The major significance of this anomaly is its association with complex cardiac defects and the associated technical difficulties at the time of cardiac catheterization and abdominal surgery or interventional procedures. In our case, we describe a common atrium and partial atrioventricular septal defect in an 8-year-old girl with infrahepatic interruption of the inferior vena cava and azygos continuation without polysplenia. Magnetic resonance angiography and computed tomography, together with a clinical awareness of this pathology, can be used to diagnose this entity.

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Dr. Bilgehan Erkut

Cardiovascular Surgery
Erzurum Training and Research Hospital
Atatürk University Medical Faculty

Kazim Karabekir Mahallesi, Teminal Caddesi,

Akgun Sitesi, 4. Block, Kat: 1, No: 4

Yenisehir/Erzurum

25080 Errzurum

Turkey

Phone: +90 50 57 80 04 83

Fax: +90 44 22 32 55 55

Email: bilgehanerkut@yahoo.com