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DOI: 10.7162/S1809-97772013000100016
Nasal paraganglioma: A case report and literature review
Publication History
29 July 2008
24 September 2012
Publication Date:
06 January 2014 (online)
![](https://www.thieme-connect.de/media/10.1055-s-00025477/201301/lookinside/thumbnails/10-7162-s-1809-97772013000100016_170116-1.jpg)
Summary
Introduction: Paragangliomas are neuroendocrine tumors that most commonly originate in the adrenal gland, a type that is called pheochromocytoma; however, 5–10% of paragangliomas are extra-adrenal and may arise in any area between the neck and pelvic region along the sympathetic nervous system. Those located in the head and neck comprise 3% of extra-adrenal tumors, with the majority originating in the tympanic–jugular region and carotid body.
Objective: To present a rare case of nasal paraganglioma and review the literature.
Case report: The patient was submitted to medial subtotal maxillectomy, and her clinical findings, diagnostic data, and treatment outcome were recorded.
Conclusion: Paragangliomas are considered benign tumors, but they occasionally display a malignant character. The most important finding in this case was the need for total resection of the tumor to avoid recurrence.
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