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Int Arch Otorhinolaryngol 2013; 17(01): 092-095
DOI: 10.7162/S1809-97772013000100016
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Nasal paraganglioma: A case report and literature review

Lídio Granato
1   Professor, Department of Otolaryngology.
,
José Donato Próspero
1   Professor, Department of Otolaryngology.
,
Dino Martini Filho
2   Associate Professor, Department of Pathological Sciences.
› Author Affiliations
Further Information

Publication History

29 July 2008

24 September 2012

Publication Date:
06 January 2014 (online)

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Summary

Introduction: Paragangliomas are neuroendocrine tumors that most commonly originate in the adrenal gland, a type that is called pheochromocytoma; however, 5–10% of paragangliomas are extra-adrenal and may arise in any area between the neck and pelvic region along the sympathetic nervous system. Those located in the head and neck comprise 3% of extra-adrenal tumors, with the majority originating in the tympanic–jugular region and carotid body.

Objective: To present a rare case of nasal paraganglioma and review the literature.

Case report: The patient was submitted to medial subtotal maxillectomy, and her clinical findings, diagnostic data, and treatment outcome were recorded.

Conclusion: Paragangliomas are considered benign tumors, but they occasionally display a malignant character. The most important finding in this case was the need for total resection of the tumor to avoid recurrence.

Keywords

Paraganglioma - Neuroendocrine Tumors - Nasal Cavity - Adrenal Gland Neoplasms - Neoplasms
 

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