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DOI: 10.5999/aps.2021.00318
Surgical management of palatal teratoma (epignathus) with the use of virtual reconstruction and 3D models: a case report and literature review
We thank Sergio Lozano MD (Scientific Publication Support Coordinator, University Hospital “Dr. José Eleuterio González”, Autonomous University of Nuevo Leon, Monterrey, Nuevo Leon, Mexico) for his review of the manuscript, and the patient, the patient´s mother, and the hospital staff for their help. Also, we thank Hernan Chacon-Moreno MD (Professor of Plastic, Aesthetic and Reconstructive Surgery Service, University Hospital “Dr. José Eleuterio González”, and Faculty of Medicine, Autonomous University of Nuevo Leon, Monterrey, Nuevo Leon, Mexico) for all the facilities provided to carry out this work.
Epignathus is a rare congenital orofacial teratoma that arises from the sphenoid region of the palate or the pharynx. It occurs in approximately 1:35,000 to 1:200,000 live births representing 2% to 9% of all teratomas. We present the case of a newborn of 39.4 weeks of gestation with a tumor that occupied the entire oral cavity. The patient was delivered by cesarean section. Oral resection was managed by pediatric surgery. Plastic surgery used virtual 3-dimensional models to establish the extension, and depth of the tumor. Bloc resection and reconstruction of the epignathus were performed. The mass was diagnosed as a mature teratoma associated with cleft lip and palate, nasoethmoidal meningocele that conditions hypertelorism, and a pseudomacrostoma. Tridimensional technology was applied to plan the surgical intervention. It contributed to a better understanding of the relationships between the tumor and the adjacent structures. This optimized the surgical approach and outcome.
Keywords
Teratoma - Pediatric plastic surgery - 3D reconstruction computed tomography - Improved surgical approachPublication History
Received: 10 February 2021
Accepted: 27 May 2021
Article published online:
19 March 2022
© 2021. The Korean Society of Plastic and Reconstructive Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonCommercial License, permitting unrestricted noncommercial use, distribution, and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes. (https://creativecommons.org/licenses/by-nc/4.0/)
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