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CC BY-NC-ND 4.0 · Eur J Dent 2015; 09(01): 153-158
DOI: 10.4103/1305-7456.149670
Review Article
Dental Investigation Society

Genetic background of supernumerary teeth

Aslı Subasioglu
1   Department of Medical Genetics, Izmir Katip Celebi University, Ataturk Training and Research Hospital, Izmir, Turkiye
,
Selcuk Savas
2   Department of Pedodontics, Dentistry Faculty, Izmir Katip Celebi University, Izmir, Turkiye
,
Ebru Kucukyilmaz
2   Department of Pedodontics, Dentistry Faculty, Izmir Katip Celebi University, Izmir, Turkiye
,
Servet Kesim
3   Department of Periodontology, Faculty of Dentistry, Erciyes University, Kayseri, Turkiye
,
Ahmet Yagci
4   Department of Orthodontics, Faculty of Dentistry, Erciyes University, Kayseri, Turkiye
,
Munis Dundar
5   Department of Medical Genetics, Medical Faculty, Erciyes University, Kayseri, Turkiye
› Author Affiliations
Further Information

Publication History

Publication Date:
04 September 2019 (online)

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ABSTRACT

Supernumerary teeth (ST) are odontostomatologic anomaly characterized by as the existence excessive number of teeth in relation to the normal dental formula. This condition is commonly seen with several congenital genetic disorders such as Gardner's syndrome, cleidocranial dysostosis and cleft lip and palate. Less common syndromes that are associated with ST are; Fabry Disease, Ellis-van Creveld syndrome, Nance-Horan syndrome, Rubinstein-Taybi Syndrome and Trico–Rhino–Phalangeal syndrome. ST can be an important component of a distinctive disorder and an important clue for early diagnosis. Certainly early detecting the abnormalities gives us to make correct management of the patient and also it is important for making well-informed decisions about long-term medical care and treatment. In this review, the genetic syndromes that are related with ST were discussed.

Key words:

Dental anomalies - genetic syndromes - supernumerary teeth
 

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