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CC BY-NC-ND 4.0 · Journal of Digestive Endoscopy 2014; 05(04): 168-170
DOI: 10.4103/0976-5042.150672
DOI: 10.4103/0976-5042.150672
Case Report
A case of cutaneous scleroderma with primary sclerosing cholangitis
Further Information
Publication History
Publication Date:
26 September 2019 (online)
Abstract
Sclerosing cholangitis comprises of a spectrum of cholestatic conditions that are characterized by patchy fibrosis, inflammation and destruction of intra hepatic and extrahepatic ducts. We report a case of a 42 year old woman who presented with darkening of skin with yellowish discolouration of the eyes. Clinical examination revealed icterus, taut skin with hepatosplenomegaly. Liver function tests showed a cholestatic picture. Skin biopsy showed features of cutaneous scleroderma. MRCP and Liver biopsy was suggestive of sclerosing cholangitis.
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