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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2008; 18(04): 298-301
DOI: 10.4103/0971-3026.43844
Musculoskeletal Radiology

Case Report: Macrodystrophia lipomatosa - Illustration of two cases

V Singla
Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
V Virmani
Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
P Tuli
Department of Plastic surgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
P Singh
Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
,
N Khandelwal
Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Macrodystrophia lipomatosa is a rare cause of congenital macrodactyly, characterized by progressive proliferation of all mesenchymal elements, with a disproportionate increase in fibroadipose tissue. This developmental anomaly is reportedly more common in the foot than in the hand, with a predilection for the plantar and median nerve distribution. We present two cases of MDL of the hand, one of which had an unusual nerve territory distribution, making clinical diagnosis difficult. Preoperative diagnosis was however made on the basis of radiography and MRI and was later confirmed on surgery.

Keywords

Macrodystrophia lipomatosa - macrodactyly - imaging


Publication History

Article published online:
31 July 2021

© 2008. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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