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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2016; 26(03): 364-372
DOI: 10.4103/0971-3026.190420
Pediatric

The Abernethy malformation-myriad imaging manifestations of a single entity

Authors

  • Samarjit S Ghuman

    Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

  • Saumya Gupta

    Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

  • T B S Buxi

    Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

  • Kishan S Rawat

    Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

  • Anurag Yadav

    Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

  • Naimish Mehta

    Department of Surgical Gastroenterology, Sir Gangaram Hospital, New Delhi, India

  • Seema Sud

    Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India

Financial support and sponsorship Nil.
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Abstract

Abernethy malformation, also known as congenital extrahepatic portosystemic shunts (CEPS) is a rare clinical entity and manifests with different clinical symptoms. CEPS are abnormalities of vascular development where there is shunting of portal blood into the systemic venous system. Multidetector computed tomography (MDCT) is a fast and effective modality for evaluation of CEPS. CT displays all the information desired by the surgeon as well as the clinician including the anatomy of the splenic and superior mesenteric veins, size and site of the shunt, presence or absence of the portal vein radicles, and helps to plan the therapy and even the follow-up of these patients. Contrast-enhanced magnetic resonance imaging (MRI) has also emerged as a promising tool for the evaluation of liver lesions associated with the malformation. The Radiologist should be aware of the various imaging appearances of this entity including its complications. In this article, we describe the imaging appearances of CEPS, their complications, and their imaging appearances on CT and MRI. We have also described various associated anomalies.

Keywords

Abernethy malformation - congenital extrahepatic portosystemic shunts - portosystemic shunts


Publikationsverlauf

Artikel online veröffentlicht:
30. Juli 2021

© 2016. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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