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DOI: 10.3233/JPN-140667
Kikuchi-Fujimoto's disease presenting as acute cerebellar ataxia
Verantwortlicher Herausgeber dieser Rubrik:
Publikationsverlauf
20. Mai 2014
12. Juni 2014
Publikationsdatum:
30. Juli 2015 (online)
Abstract
Kikuchi-Fujimoto disease (KFD) is a benign and self-limiting condition primarily affecting the cervical lymph nodes. Central nervous system involvement with acute cerebellar symptoms is a rare presentation in KFD. We report a 15-year-old girl presenting with intentional tremor, dysarthria and gait ataxia following episodes of recurrent fever and cervical lymphadenopathy. The diagnosis of KFD was made based on histopathology. Brain magnetic resonance imaging showed lesions in mid-pons and bilateral middle cerebellar peduncles. The patient's symptoms spontaneously resolved without any sequelae. A diagnosis of KFD should be considered when enlarged cervical lymphnodes are observed in patients with acute cerebellar symptoms. Selective inflammation of cerebellum and related structures by viral or immunological responses may be attributed to this rare presentation in KFD.