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Am J Perinatol 2008; 25(2): 125-128
DOI: 10.1055/s-2007-1004832
DOI: 10.1055/s-2007-1004832
Sildenafil Use in a Symptomatic Neonate with Severe Ebstein's Anomaly of the Tricuspid Valve
Further Information
Publication History
Publication Date:
19 December 2007 (online)
ABSTRACT
Ebstein's anomaly (EA) is associated with poor outcome in symptomatic neonates. Management typically includes prostaglandins or surgical creation of a Blalock-Taussig shunt. Right ventricular afterload reduction may help by improving the forward flow across the pulmonary valve. We report the successful use of oral sildenafil, a pulmonary vasodilator, in a neonate with severe EA.
KEYWORDS
Ebstein's anomaly - sildenafil - cyanosis - neonate
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Sanjeev AggarwalM.D.
Division of Cardiology, The Carman and Ann Adams Department of Pediatrics, Children's Hospital of Michigan, Wayne State University
3901 Beaubien Blvd, Detroit, MI 48201