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DOI: 10.1055/s-2004-828705
Copyright © 2004 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA.
Malignant Peripheral Nerve Sheath Tumor of the Orbit: Case Report and Literature Review
Publication History
Publication Date:
04 June 2004 (online)
![](https://www.thieme-connect.de/media/sbs/200402/lookinside/thumbnails/10.1055-s-2004-828705-1.jpg)
A 68-year-old woman with progressive visual loss and exophthalmos in her right eye had been operated on for a mass in her right calf 3 years earlier. Imaging showed a huge mass invading the orbital structures and temporal pole. The presumptive diagnosis was a malignant orbital tumor. The tumor was resected totally and eroded tissues such as the lateral rectus muscle and dural compartments were repaired. The histological diagnosis was a malignant peripheral nerve sheath tumor (MPNST). The patient recovered uneventfully and was discharged 8 days after surgery. Two years later she died from a liver tumor. Few MPNSTs involving the orbit have been reported.
KEYWORDS
Malignant peripheral nerve sheath tumor - orbit
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Dr
Mehmet D Aydin
Atatürk Üniversitesi Lojmanlari
60 Blok, Kat 1, No. 3, Erzurum, Turkey
Email: nmda21@hotmail.com