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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2024; 34(01): 172-176
DOI: 10.1055/s-0043-1774392
Case Report

Very Rare Liver Tumor: PEComa Case Report with and a Review of Literature

Celal Yazıcı 
1   Department of Radiology, Eskişehir Osmangazi University, Faculty of Medicine, Eskişehir, Turkey
,
Elif Gündoğdu 
1   Department of Radiology, Eskişehir Osmangazi University, Faculty of Medicine, Eskişehir, Turkey
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Abstract

Perivascular epithelioid cell tumors (PEComas) are very rare mesenchymal tumors. In addition to being rare in general, they are even rarer in the liver. There are various subtypes and there is only one case of liver PEComa reported in the clear cell type in the literature to date. We present the second clear cell type liver PEComa in this case by reviewing the literature data. The hypodense, smooth-edged, ovoid lesion was detected on computed tomography (CT) for performing abdominal pain in a 41-year-old female patient. Magnetic resonance imaging (MRI) was then performed for lesion characterization. The lesion was hypointense on T1-weighted imaging (T1WI), hyperintense on T2-weighted imaging (T2WI). In dynamic phases, it showed marked enhancement on the arterial phase and capsular enhancement with central washout on the portal and late venous phases. The posterior branch of the right portal vein extended into the mass. The lesion was excised and the pathological result was epithelioid clear cell subtype of PEComa. Although the imaging findings are generally nonspecific and certain diagnosis is made histopathologically, radiologists should consider PEComa in the differential diagnosis in the presence of intensely enhanced lesion on the right lobe in female patients. Also, the “large vessel sign” may help in the diagnosis.

Keywords

perivascular epithelioid cell tumors liver - computer tomography - magnetic resonance imaging

Author Contributions

C.Y. was responsible for the conceptualization, data curation, investigation, and writing the original draft. E.G. was responsible for formal analysis, investigation, review, supervision, and editing.


Consent for Publication

Informed consent was obtained from the patient prior to the study.




Publication History

Article published online:
27 October 2023

© 2023. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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