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CC BY-NC-ND 4.0 · Journal of Gastrointestinal and Abdominal Radiology 2023; 06(01): 071-076
DOI: 10.1055/s-0042-1758125
Case Report

Case Report of Undifferentiated Hepatic Embryonal Sarcoma with Mesenchymal Hamartoma: A Rare Entity

Dhanya Jacob
1   Department of Radiology, VPS Lakeshore Hospital, Kochi, Kerala, India
,
Thara Pratap
1   Department of Radiology, VPS Lakeshore Hospital, Kochi, Kerala, India
,
Abhishek Yadav
2   Department of Comprehensive Liver Care, VPS Lakeshore Hospital, Kochi, Kerala, India
,
Muhammed Jasim Abdul Jalal
3   Department of Internal Medicine and Rheumatology, VPS Olive Healthcare, Thrissur, Kerala, India
,
Pushpa Mahadevan
4   Department of Pathology, VPS Lakeshore Hospital, Kochi, Kerala, India
,
Reshmi Unnikrishnan
5   Department of Paediatrics, VPS Lakeshore Hospital, Kochi, Kerala, India
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Abstract

Undifferentiated embryonal sarcoma (UES) is a highly malignant hepatic neoplasm, which occurs mostly in pediatric population. There is a link between embryonal sarcoma and mesenchymal hamartoma as evidenced by clinicopathological overlap and similar genetic abnormality. Here, we report a case of UES in a young female in a background of mesenchymal hamartoma of liver.

Keywords

abdominal pain - alpha-fetoprotein - hepatomegaly - mesenchymal hamartoma - undifferentiated embryonal sarcoma


Publication History

Article published online:
09 December 2022

© 2022. Indian Society of Gastrointestinal and Abdominal Radiology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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