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CC BY-NC-ND 4.0 · Asian J Neurosurg 2022; 17(03): 532-535
DOI: 10.1055/s-0042-1756637
Case Report

Diffuse Leptomeningeal Glioneuronal Tumor: A Rare Case Report with Review of Literature

Amey P. Patankar
1   Department of Neurosurgery, Baroda Medical College and SSG Hospital, Vadodara, Gujarat, India
,
Palak Vaghela
2   Department of Radiology, Sahyog Imaging Centre, Vadodara, Gujarat, India
,
Jitendra Nasit
3   Department of Pathology, Baroda Medical College and SSG Hospital, Vadodara, Gujarat, India
,
Rajvee Gohil
4   Department of Surgery, Baroda Medical College and SSG Hospital, Vadodara, Gujarat, India
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Abstract

Diffuse leptomeningeal glioneuronal tumor (DLGNT) is a rare tumor that was defined as a separate entity in the 2016 World Health Organization classification of brain tumors. It is most common in the pediatric age group. The diagnosis of this tumor can be made preoperatively by its characteristic imaging findings of diffuse intracranial and intraspinal nodular leptomeningeal thickening and enhancement associated with small cyst-like nonenhancing lesions in the brain and spinal cord. We report a case of DLGNT in a 7-year-old male presenting with hydrocephalus. The patient was treated successfully by cerebrospinal fluid (CSF) diversion followed by biopsy of the lesion from the cerebellum. Histopathology and immunohistochemistry confirmed the diagnosis of DLGNT. Our case would hopefully increase the awareness regarding this rare tumor and facilitate an early diagnosis and management of the affected patients with atypical radiological features.

Keywords

glioneuronal tumor - diffuse glioneuronal leptomeningeal tumor - pediatric brain tumor - WHO classification of brain tumor - glial tumor

Note

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Publication History

Article published online:
08 October 2022

© 2022. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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