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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2023; 33(03): 394-399
DOI: 10.1055/s-0041-1741092
Case Series

Multimodality Imaging Appearance of Intrapericardial Paragangliomas

Diana Palacio
,
Maria del Pilar Gutierrez
2   Department of Radiology, Universidad de Antioquia-Facultad de Medicina, Tucson, Arizona, United States
,
Gokhan Kuyumcu
1   Department of Medical Imaging, The University of Arizona College of Medicine, Tucson, Arizona, United States
,
Benjamin Rounseville
1   Department of Medical Imaging, The University of Arizona College of Medicine, Tucson, Arizona, United States
,
Volodymyr Shponka
3   Department of Pathology, The University of Arizona College of Medicine, Tucson, Arizona, United States
,
Sonia Betancourt
4   Department of Radiology, The University of Texas MD Anderson Cancer Center, Tucson, Arizona, United States
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Abstract

Paragangliomas are neuroendocrine tumors of the sympathetic and parasympathetic nervous system that originate from neural crest cells. Less than 1% of paragangliomas are found in the heart, originating from intrinsic cardiac ganglia cells in the posterior wall the atria, atrioventricular groove, and along the root of the great vessels. A 10-year review of our institution's database identified nine patients who had documented intrapericardial paragangliomas. We describe the multimodality imaging appearance of these tumors. The most common findings include embedment and wrapping around the great vessels and atrioventricular groove within the confines of the pericardium, markedly avid heterogeneous enhancement, distinct engorged neovascularization, and in large lesions, central low attenuation areas compatible with hemorrhage, necrosis, or cystic degeneration.

Keywords

chest imaging - intrapericardial paragangliomas - multidetector computed tomography

Supplementary Material



Publication History

Article published online:
31 January 2023

© 2023. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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