Focal Ballismus (Right Arm) in a Boy with Wilson's Disease

Abstract

Ballismus is defined as rapid, forceful, shaking or throwing involuntary movement of the extremities, mainly proximal parts. When it affects half of the body (upper and lower limbs on one side), it is called hemiballismus. If it affects one limb, it could be labeled as focal or one limb ballismus. Any lesion (vascular, trauma, tumor, deposition, and demyelination) in the subthalamic nucleus of the basal ganglia results in ballismus. A rare entity such as copper deposition in Wilson's disease can manifest as ballismus. In this case report, we described a boy with Wilson's disease with focal ballismus of the right arm.

Keywords

chorea - dystonia - ballismus - Wilson's disease

Note

The preparation of this manuscript was not supported by any grant, was presented in the departmental meeting. This is not under consideration of publication anywhere else. All the coauthors have seen and approved the final version of the manuscript and agree to share any material used in the experiments or videotapes.

Publication History

Received: 13 June 2020

Accepted: 03 July 2020

Article published online:
26 August 2020

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