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J Hand Microsurg 2022; 14(03): 255-259
DOI: 10.1055/s-0040-1714452
Case Report

Bilateral Preiser Disease in a Patient with Sickle Cell Anemia

Joseph Catapano
1   Division of Plastic and Reconstructive Surgery, University of Toronto, Toronto, Ontario, Canada
2   Toronto Western Hospital, University Health Network, Toronto, Ontario, Canada
,
Oluwatola O. Overduin
2   Toronto Western Hospital, University Health Network, Toronto, Ontario, Canada
,
Herbert P. von Schroeder
1   Division of Plastic and Reconstructive Surgery, University of Toronto, Toronto, Ontario, Canada
2   Toronto Western Hospital, University Health Network, Toronto, Ontario, Canada
3   Division of Orthopedic Surgery, The University of Toronto, Toronto, Ontario, Canada
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Abstract

Preiser disease is a rare condition of avascular necrosis of the scaphoid occurring in the absence scaphoid fracture or trauma. While the etiology of Preiser disease remains unknown, it has been associated with steroid use, chemotherapy, and infrequently with systemic diseases. No reports have associated Preiser disease with hemoglobinopathy. Due to the rarity of Preiser disease, management remains controversial and evidence is limited. Here, we describe the case of a 32-year-old right-hand dominant male with sickle cell anemia and a 4-year history of bilateral wrist pain. Radiographs and gadolinium-enhanced magnetic resonance imaging revealed bilateral Preiser disease. He was successfully managed with a 1,2 intercompartmental supraretinicaular artery vascularized bone graft to the right scaphoid.

Keywords

Preiser disease - hemoglobinopathy - sickle cell disease - vascularized bone grafts


Publication History

Article published online:
10 August 2020

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