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CC BY 4.0 · Rev Bras Ginecol Obstet 2020; 42(05): 297-302
DOI: 10.1055/s-0040-1710350
Case Report
Thieme Revinter Publicações Ltda Rio de Janeiro, Brazil

Desmoplastic Small Round Cell Tumor of the Ovary: A Case Report with a New Modality of Treatment and Review of the Literature

Goran Vujić 
1   Department of Obstetrics and Gynecology, University Hospital Center Zagreb, Zagreb, Croatia
,
Mislav Mikuš 
1   Department of Obstetrics and Gynecology, University Hospital Center Zagreb, Zagreb, Croatia
,
Luka Matak 
2   Department of Obstetrics and Gynecology, General Hospital Zadar, Zadar, Croatia
,
Aleksandra Bonevski 
3   Department of Oncology and Hematology, Children's Hospital Zagreb, Zagreb, Croatia
,
Ivan Babić 
1   Department of Obstetrics and Gynecology, University Hospital Center Zagreb, Zagreb, Croatia
,
Pavao Planinić 
1   Department of Obstetrics and Gynecology, University Hospital Center Zagreb, Zagreb, Croatia
,
Damir Babić 
1   Department of Obstetrics and Gynecology, University Hospital Center Zagreb, Zagreb, Croatia
,
Ante Ćorušić 
1   Department of Obstetrics and Gynecology, University Hospital Center Zagreb, Zagreb, Croatia
› Author Affiliations
Further Information

Publication History

15 July 2019

02 March 2020

Publication Date:
29 May 2020 (online)

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Abstract

Objective Desmoplastic small round cell tumor (DSRCT) is a rare intraabdominal neoplasm that grows along serosal surfaces and is primarily found in young men. To date, only 16 cases of ovarian DSRCT have been previously reported in women in the English literature, and no large population-based studies on this topic exist.

Case Report We report the case of a 19-year-old virgo with unremarkable past medical history, initially presented with abdominal fullness. After being treated with the optimal treatment modality (primary and secondary surgical debulking, unique chemotherapy, protocol and adjuvant radiotherapy), the patient has remained without tumor disease for 40 months.

Conclusion Although the best therapy for patients with DSRCT has yet to be determined, combining complete surgical resection, adjuvant chemotherapy, and radiotherapy is required to prolong survival and to achieve proper quality of life.

Keywords

desmoplastic small round cell tumor - ovary - surgical debulking - adjuvant chemotherapy - radiotherapy - immunohistochemistry
 

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