Anesthetic Management of a Case of Vein of Galen Aneurysmal Malformation

Background: A vein of Galen aneurysmal malformation is a rare congenital arteriovenous malformation of intracranial circulation in and causes intractable congestive high-output cardiac failure in a neonate. Atrial septal defect is a common congenital cardiac anomaly resulting from a defect in the interatrial septum that causes shunting of blood from the left atrium to the right atrium through the defect leading to enlargement of the right side of the heart and of the pulmonary arteries.

Case Description: We present a case of vein of Galen malformation associated with atrial septal defect and its associated complications planned for embolization. A 9-month-old infant was brought with complaints of increasing head size and an uneventful birth history. MRI was done and vein of Galen malformation was diagnosed. Chest X-ray showed cardiomegaly and echocardiogram revealed severe atrial septal defect with right atrial and right ventricular enlargement. The infant was apparently normal with no significant events.

Conclusion: Embolization was done under general anesthesia and the patient was hemodynamically stable during the perioperative and postoperative period. The case was challenging because of its association with severe atrial septal defect

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Artikel online veröffentlicht:
25. März 2020