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CC BY 4.0 · European J Pediatr Surg Rep. 2019; 07(01): e117-e120
DOI: 10.1055/s-0039-3399557
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Successful Brace Treatment of Pectus Carinatum in Osteogenesis Imperfecta Using the Dynamic Compression System

Beth A. Orrick
1   Department of Pediatric Surgery, Center for Pectus Excavatum and Carinatum, Children's Mercy Hospital, Kansas City, Missouri, United States
,
Amy L. Pierce
1   Department of Pediatric Surgery, Center for Pectus Excavatum and Carinatum, Children's Mercy Hospital, Kansas City, Missouri, United States
,
Charles L. Snyder
1   Department of Pediatric Surgery, Center for Pectus Excavatum and Carinatum, Children's Mercy Hospital, Kansas City, Missouri, United States
,
Uri S. Alon
2   Bone and Mineral Disorders Clinic, Division of Pediatric Nephrology, Children's Mercy Hospital, Kansas City, Missouri, United States
› Author Affiliations
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Publication History

03 July 2019

25 September 2019

Publication Date:
31 December 2019 (online)

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Abstract

Osteogenesis imperfecta (OI) is a genetic disorder of collagen resulting in a “fragile” skeleton with increased fracture risk and other complications, dependent on the specific variant. Pectus deformities of the chest wall, while not common, can be associated with OI. The use of a pectus carinatum brace in a patient with OI poses unknown risks for fractures and adverse treatment outcomes. We successfully applied external compression bracing using the dynamic compression system to one such patient. This case illustrates the ability to treat an OI patient with pectus carinatum using a nonsurgical brace, without complications, resulting in an excellent cosmetic result.

Keywords

pectus carinatum - osteogenesis imperfecta - dynamic compression system
 

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