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CC BY 4.0 · European J Pediatr Surg Rep. 2019; 07(01): e16-e19
DOI: 10.1055/s-0039-1692154
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Fatal Course of Abdominal Neonatal Intestinal Fibrosarcoma

Béatrice Boutillier 
1   Department of Radiology, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Liesbeth Cardoen
1   Department of Radiology, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Marianne Alison
1   Department of Radiology, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Dominique Berrebi
2   Department of Anatomopathology, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Jonathan Rosenblatt
3   Department of Gynecology and Obstetrics, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Anne-Laure Virlouvet
4   Department of Neonatology and Intensive Care Unit, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Jean Michon
5   Department of Pediatric Oncology, Institut Curie, Paris, Île-de-France, France
,
Sophie Soudée
4   Department of Neonatology and Intensive Care Unit, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
,
Arnaud Bonnard
6   Department of Pediatric Surgery and Urology, Robert-Debré University Hospital, Assistance-Publique Hôpitaux de Paris, Paris, Île-de-France, France
7   UMR 1149 Inserm Universite Paris Diderot, Sorbonne Paris Cité, Paris, Île-de-France, France
› Author Affiliations
Further Information

Publication History

19 June 2018

28 April 2019

Publication Date:
09 June 2019 (online)

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Abstract

Infantile fibrosarcoma (IFS) is a rare nonrhabdomyosarcoma soft tissue tumor and accounts for less than 1% of childhood cancers. Forty per cent are present at birth and only 10% of IFS occurs in the abdomen. Our case of neonatal fibrosarcoma presented as a distal small bowel stenosis complicated with meconium peritonitis. The diagnosis was by histology of the surgical resection. The diagnosis of IFS is challenging as there are no specific features of IFS on imaging. Any unexpected solid lesion should raise the suspicion of complicated bowel tumoral lesion. If a neoplastic lesion is suspected extensive, surgery may be postponed until the final diagnosis is made.

Keywords

congenital fibrosarcoma - prenatal diagnosis - MR Imaging - haemorrhagic shock - meconium peritonitis
 

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