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Nervenheilkunde 2005; 24(09): 801-808
DOI: 10.1055/s-0038-1630011
Original Article
Schattauer GmbH

Frontotemporale lobäre Degenerationen

Frontotemporal lobar degenerations
J. Diehl
1   Klinik und Poliklinik für Psychiatrie und Psychotherapie der TU München (Leiter: Prof. Dr. H. Förstl)
,
H. Förstl
1   Klinik und Poliklinik für Psychiatrie und Psychotherapie der TU München (Leiter: Prof. Dr. H. Förstl)
,
A. Kurz
1   Klinik und Poliklinik für Psychiatrie und Psychotherapie der TU München (Leiter: Prof. Dr. H. Förstl)
› Author Affiliations
Further Information

Publication History

Eingegangen am: 17 May 2005

angenommen am: 21 June 2005

Publication Date:
24 January 2018 (online)

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Zusammenfassung

Die frontotemporalen lobären Degenerationen (FTLD) stellen die Ursache unterschiedlicher und vielfältiger psychiatrischer und neurologischer Störungen dar. In der vorliegenden Übersichtsarbeit werden die einzelnen klinischen Syndrome vorgestellt, die genetischen und pathologischen Grundlagen erläutert, die derzeitigen Möglichkeiten der Diagnostik vorgestellt und Therapieoptionen aufgezeigt.

Summary

Frontotemporal degenerations cause various clinical psychiatric and neurological syndromes. This review introduces the clinical syndromes, genetic basis and pathological variability, diagnostic procedures and therapeutic strategies.

Schlüsselwörter

Pick-Krankheit - frontotemporale Demenz - Aphasie - Blickparese - kortikobasale Degeneration - amyotrophe Lateralsklerose

Keywords

Pick’s disease - frontotemporal dementia - aphasia - corticobasal degeneration - propalsy - motor neuron disease
 

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