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Hamostaseologie 2003; 23(04): 170-180
DOI: 10.1055/s-0037-1619594
Original Article
Schattauer GmbH

Angeborene und erworbene Thrombozytenfunktionsstörungen

Congenital and acquired platelet functional disorders
R. E. Scharf
1   Institut für Hämostaseologie und Transfusionsmedizin, Universitätsklinikum, Heinrich-Heine-Universität Düsseldorf
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Further Information

Publication History

Publication Date:
20 January 2018 (online)

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Zusammenfassung

Es wird ein Überblick über angeborene und erworbene Thrombozytenfunktionsstörungen und ihre Therapiemöglichkeiten gegeben. Angeborene Thrombozytenfunktionsstörungen kommen extrem selten vor, erworbene Störungen hingegen dürften die häufigsten Störungen der Blutstillung sein. Die Aufklärung der den angeborenen Störungen zugrunde liegenden Defekte hat unser Verständnis der Plättchenfunktionen wesentlich verbessert. Erworbene Plättchenfunktionsstörungen werden durch unterschiedlichste Erkrankungen oder Arzneimittel hervorgerufen.

Summary

A survey is given on congenital and acquired platelet functional disorders. Congenital platelet functional disorders are extremely rare. Acquired platelet functional disorders are probably the most frequent disturbances of haemostasis. The knowledge of the defects leading to inherited platelet function disorders much improved our understanding of platelet function in general. Acquired platelet functional disorders are due to various diseases and drugs.

Schlüsselwörter

Thrombozytopathien

Keywords

Platelet functional disorders
 

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