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European J Pediatr Surg Rep. 2016; 04(01): 001-005
DOI: 10.1055/s-0035-1570370
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Caudal Duplication Syndrome: the Vital Role of a Multidisciplinary Approach and Staged Correction

Inbal Samuk
1   Department of Pediatric Surgery, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
,
Marc Levitt
2   Center for Colorectal and Pelvic Reconstruction, Nationwide Children's Hospital, Columbus, Ohio, United States
,
Elena Dlugy
1   Department of Pediatric Surgery, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
,
Dragan Kravarusic
1   Department of Pediatric Surgery, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
,
David Ben-Meir
3   Pediatric Urology Unit, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
,
Gustavo Rajz
4   Pediatric Neurosurgery Unit, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
,
Osnat Konen
5   Radiology Department, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
,
Enrique Freud
1   Department of Pediatric Surgery, Schneider Children's Medical Center, Sackler Medical School, University of Tel Aviv, Petach Tikvah, Israel
› Author Affiliations
Further Information

Publication History

16 August 2015

09 November 2015

Publication Date:
31 December 2015 (online)

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Abstract

Caudal duplication syndrome is a rare entity that describes the association between congenital anomalies involving caudal structures and may have a wide spectrum of clinical manifestations. A full-term male presented with combination of anomalies including anorectal malformation, duplication of the colon and lower urinary tract, split of the lower spine, and lipomyelomeningocele with tethering of the cord. We report this exceptional case of caudal duplication syndrome with special emphasis on surgical strategy and approach combining all disciplines involved. The purpose of this report is to present the pathology, assessment, and management strategy of this complex case.

Keywords

caudal duplication syndrome - anorectal malformation - rectal duplication - colonic duplication - genitourinary duplication
 

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