An unusual cause of ankle swelling

Introduction

Primary Intestinal Lymphangiectasia (PIL) is a rare idiopathic congenital disorder characterized by impaired lymphatic drainage and protein-losing enteropathy [1] [2].

PIL normally presents in childhood but can unusually present in adults [2]. We report a case of PIL diagnosed at antegrade double-balloon enteroscopy in a middle-aged man with isolated intermittent ankle edema and hypoalbuminemia.

• References

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