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Z Geburtshilfe Neonatol 2013; 217(06): 204-210
DOI: 10.1055/s-0033-1355359
Review
© Georg Thieme Verlag KG Stuttgart · New York

Review on Current Management and Outcome Data of Echogenic Lung Lesions and Hydrothorax of the Fetus

Aktuelles Management und Outcome von fetalen echogenen Lungenläsionen und Hydrothorax
J. Degenhardt
1   Division of Prenatal Medicine, Department of OB/GYN, Justus-Liebig-University, Giessen, Germany
,
T. Kohl
2   German Center for Fetal Surgery & Minimally Invasive Therapy (DZFT), Justus-Liebig-University, Giessen, Germany
,
C. Enzensberger
1   Division of Prenatal Medicine, Department of OB/GYN, Justus-Liebig-University, Giessen, Germany
,
R. Axt-Fliedner
1   Division of Prenatal Medicine, Department of OB/GYN, Justus-Liebig-University, Giessen, Germany
› Author Affiliations
Further Information

Publication History

received 12 January 2013

accepted 22 August 2013

Publication Date:
20 December 2013 (online)

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Abstract

This review focuses on the prenatal management and outcome of echogenic lung lesions and isolated hydrothorax of the fetus. We give an overview of the most common forms of echogenic lung lesions like cystic adenomatoid malformation of the lung and bronchopulmonary sequestration as well as of congenital high airway obstruction sequence. We review the occurrence, appearance, pathophysiology and natural history of these lesions. Furthermore we discuss selection criteria for intrauterine treatment and algorithms for prenatal surveillance of affected fetuses.

Zusammenfassung

Die Arbeit bietet eine Übersicht über das pränatale Management und aktuelle Outcomedaten von Feten mit echogenen Lungenläsionen und Feten mit Hydrothorax. Wir berichten über die häufigsten Formen echogener Lungenläsionen (cystisch adenomatoide Lungenmalformation, bronchopulmonale Sequestration sowie die Congenital High Airway Obstruction Sequence) und geben einen Überblick über Auftreten, pränatale Diagnose und die Pathophysiologie der Malformation. Außerdem diskutieren wir Selektionskriterien für eine pränatale Therapie und stellen Behandlungspfade für die intrauterine Überwachung betroffener Feten vor.

Key words

echogenic lung lesions - hydrothorax - congenital high airway obstruction sequence - cystic adenomatoid ­malformation - bronchopulmonary ­sequestration

Schlüsselwörter

echogene Lungenläsionen - Hydrothorax - congenital high airway obstruction sequence - cystisch adenomatoide Lungenmalformation - bronchopulmonale ­Sequestration
 

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