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Eur J Pediatr Surg 2013; 23(01): 072-075
DOI: 10.1055/s-0032-1330841
Original Article
Georg Thieme Verlag KG Stuttgart · New York

A Proposed Classification for the Spectrum of Vanishing Gastroschisis

Tarun Kumar
1   Department of Surgery, School of Osteopathic Medicine, Des Moines University, Des Moines, Iowa, United States
,
Richard Vaughan
2   Department of Surgery, Robert C. Byrd Health Science Center, West Virginia University, Morgantown, West Virginia, United States
,
Mark Polak
3   Department of Pediatrics, Robert C. Byrd Health Science Center, West Virginia University, Morgantown, West Virginia, United States
› Author Affiliations
Further Information

Publication History

31 March 2012

17 September 2012

Publication Date:
21 November 2012 (online)

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Abstract

Infants born with gastroschisis in association with intestinal atresia are well described. We are the proposing the classification of vanishing gastroschisis. In this series of six cases, at one end of the spectrum is an infant having gastroschisis with a much narrower defect on the right side of umbilicus. The ischemic bowel loops were connected to bowel inside the abdomen by a fibrous band compressing the exposed bowel mesentery. On the other end of spectrum, an infant having extensive bowel atresia and complete closure of abdominal wall defect (gastroschisis) detected on antenatal ultrasound. These cases should raise awareness of this devastating complication in prenatal management of gastroschisis.

Keywords

gastroschisis - intestinal atresia - abdominal wall defect - vanishing gut
 

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