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Neuropediatrics 2013; 44(03): 171-173
DOI: 10.1055/s-0032-1329908
DOI: 10.1055/s-0032-1329908
Short Communication
Isolated Intraspinal Juvenile Xanthogranuloma in an Infant Presenting as Acute Paraplegia
Weitere Informationen
Publikationsverlauf
25. Juni 2012
01. Oktober 2012
Publikationsdatum:
19. Dezember 2012 (online)
![](https://www.thieme-connect.de/media/neuropediatrics/201303/lookinside/thumbnails/10.1055-s-0032-1329908-1.jpg)
Abstract
Juvenile xanthogranuloma is a histiocytic proliferative disease that predominantly affects the skin. Extracutaneous involvement is rare. We present the case of a 6-month-old infant with acute paraplegia. Magnetic resonance imaging showed an intraspinal extradural mass at midthoracic level with marked compression of the spinal cord. Complete tumor removal was achieved by emergency surgery and was followed by complete neurologic recovery. Histologic examination led to the diagnosis of a juvenile xanthogranuloma. To the best of our knowledge, an isolated intraspinal juvenile xanthogranuloma in the first 12 months of life has not been described before.
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