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Klin Monbl Augenheilkd 2013; 230(4): 346-348
DOI: 10.1055/s-0032-1328375
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Georg Thieme Verlag KG Stuttgart · New York

Ligneous Conjunctivitis in a Young Patient with Homozygous K19E Plasminogen Gene Mutation: a Diagnostic and Therapeutic Challenge

Conjunctivitis lignosa bei einer jungen Patientin mit homozygoter K19E-Mutation im Plasminogen-Gen: eine diagnostische und therapeutische Herausforderung
A. Kuonen
1   Jules Gonin Eye Hospital and University of Lausanne, Department of Ophthalmology, Lausanne, Switzerland (Chairman: Prof. L. Zografos)
,
J. Vaudaux
1   Jules Gonin Eye Hospital and University of Lausanne, Department of Ophthalmology, Lausanne, Switzerland (Chairman: Prof. L. Zografos)
,
M. Hamedani
1   Jules Gonin Eye Hospital and University of Lausanne, Department of Ophthalmology, Lausanne, Switzerland (Chairman: Prof. L. Zografos)
,
V. Schuster
4   Universitätsklinik und Poliklinik für Kinder und Jugendliche, Leipzig, Germany (Chairman: Prof. Dr. Wieland Kiess)
,
M. Albisetti
2   Division of Hematology, University Childrenʼs Hospital, Zürich, Switzerland (Chairman: Dr. Dieter von Schulthess)
,
N. von der Weid
3   Division of Hematology and Oncology, University Childrenʼs Hospital UKBB, Basel, Switzerland (Chairman: Prof. Urs Frey)
,
P.-F. Kaeser
1   Jules Gonin Eye Hospital and University of Lausanne, Department of Ophthalmology, Lausanne, Switzerland (Chairman: Prof. L. Zografos)
› Author Affiliations
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Publication History

Publication Date:
29 April 2013 (online)

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Ligneous Conjunctivitis in a Young Patient with Homozygous K19E Plasminogen Gene Mutation: a Diagnostic and Therapeutic ChallengeKlin Monbl Augenheilkd 2013; 230(07): e18-e18
DOI: 10.1055/s-0032-1328725

Background

Ligneous conjunctivitis is a chronic disease that may be triggered by ocular trauma or surgery in patients with type I plasminogen deficiency [1], [2]. In a recent review of the literature, the prevalence of type-I plasminogen deficiency is only 16 cases per 1 000 000 [1]. The hallmark of ligneous conjunctivitis is the presence of fibrin-rich pseudomembraneous lesions on tarsal conjunctivae.

 

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