Int J Angiol 2010; 19(1): e48-e50
DOI: 10.1055/s-0031-1278365
Case Report

© Georg Thieme Verlag KG Stuttgart · New York

Large pulmonary artery aneurysm associated with Marfan syndrome

Peter Ting1 , Bodh I Jugdutt2 3 , Ju Le Tan1
  • 1National Heart Centre, Singapore
  • 2Mazankowski Alberta Heart Institute, Edmonton, Alberta
  • 3University of Alberta Hospital, Edmonton, Alberta
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Publikationsverlauf

Publikationsdatum:
28. April 2011 (online)

Abstract

Pulmonary artery aneurysms are rare and published data on the subject are limited. The first case of Marfan syndrome associated with a large pulmonary artery aneurysm complicated by pulmonary artery thrombi and pulmonary hypertension is described. Serial echocardiograms showed progressive dilation of the aneurysm, which reached a massive size of 90 mm. Cardiac catheterization, pulmonary angiography and computed tomography angiography were used in the preoperative evaluation. The patient died suddenly awaiting a decision for surgical intervention, thereby underscoring the need for aggressive management.