Neuropediatrics 2011; 42 - VS07
DOI: 10.1055/s-0031-1273971

Stimulus-sensitive epilepsy, with seizures while feeding in the morning

U Kalmus 1
  • 1Christopherus Kliniken Coesfeld, Abteilung für Kinder und Jugendmedizin – Neuropädiatrie, Coesfeld, Germany

Case report: A 5 year and 2 month-old boy with partial monosomic chromosome 17, tetralogy of Fallot, and multiple surgical corrections of the heart. Every morning for approximately 6 months, he has exhibited daily, peculiar behavior while being fed porridge (cereal?). After having a few spoonfuls of porridge (cereal), the boy suddenly starts to clap his hands rapidly, and then contorts his eyes and has tonic extension of his trunk. This episode is followed by approximately 30 minutes of sleep. Afterwards, the child is clinically unremarkable. These episodes do not occur at other times of the day.

There are fewer seizures when the child receives Proton Pump Inhibitors (PPI's).

EEG while awake: focal and general irregular spike and wave pattern, as seen with Absence-type seizures.

EEG while asleep: shows hypsarrhythmia.

EEG during feeding: shows a clear seizure pattern.

Video demonstration of EEG while feeding.