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DOI: 10.1055/s-0030-1253688
© Georg Thieme Verlag KG Stuttgart · New York
Chronisch thromboembolische pulmonale Hypertension (CTPH)
Krankheitsbild und chirurgische BehandlungsmöglichkeitenChronic thromboembolic pulmonary hypertension (CTPH)Disease pattern and surgical optionsPublikationsverlauf
eingereicht: 21.10.2009
akzeptiert: 18.3.2010
Publikationsdatum:
05. Mai 2010 (online)
![](https://www.thieme-connect.de/media/dmw/201019/lookinside/thumbnails/10.1055-s-0030-1253688-1.jpg)
Zusammenfassung
Die chronisch thromboembolisch pulmonale Hypertension (CTPH) ist ein häufig unterschätztes Krankheitsbild, welches ursächlich für eine schwere pulmonale Hypertonie und Rechtsherzversagen ist. Gegenwärtig entwickelt sich bei 1 % bis 4 % der Patienten, die eine Lungenembolie überlebt haben, eine CTPH. Für den Großteil dieser Patienten stellt die pulmonale Endarteriektomie (PEA) die einzige kurative Behandlung dar. Diagnostik und Behandlung sollten aufgrund der Komplexität der Erkrankung in einem erfahrenen Zentrum durchgeführt werden.
Abstract
Chronic thromboembolic pulmonary hypertension CTPH is an important cause of severe pulmonary hypertension and right-sided heart failure, which has been under recognised in the past. Current estimates indicate that 1 % to 4 % of patients who survive a pulmonary embolus will develop CTPH. Appropriate diagnosis and assessment are vital as the majority of patients with this condition can be effectively cured with pulmonary endarterectomy (PEA). Assessment and surgical treatment of these patients should only be carried out in a centre with significant experience in treating this condition.
Schlüsselwörter
chronisch thromboembolische pulmonale Hypertension - CTPH - pulmonale Hypertonie - pulmonale Endarteriektomie - PEA
Keywords
chronic thromboembolic pulmonary hypertension - CTPH - pulmonary endarterectomy - PEA
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