Prenatal Ultrasound Diagnosis of a Multiple Atypical Right Atrial Cardiac Fibroma

Introduction

Congenital cardiac tumors are very rare with an incidence at birth of approximately 0.0017 – 0.28 % (Holly DG et al. J Am Coll Cardiol 1995; 26: 516 – 520). The majority of cardiac tumors in children are benign, with only approximately 10 % being malignant. The manifestations of a cardiac tumor in fetal life include congestive heart failure, arrhythmias, hydrops and sudden death (Allan L. In Textbook of Fetal Cardiology: Greenwich Medical Media, London, 2000; 358 – 365; Atallah J et al. Pediatr Cardiol 2006; 27: 493 – 496).

We report a case with an atypical form of cardiac fibroma located in the right atrium. To the best of our knowledge a cardiac fibroma located in the right atrium has not previously been reported in the literature. The prenatal diagnosis was made at 36 weeks of gestation.

1 VVI is a pacemaker that senses and stimulates in the ventricle alone and is inhibited by spontaneous electrical activity in the ventricle.