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DOI: 10.1055/s-0029-1243171
© Georg Thieme Verlag KG Stuttgart · New York
Aplasia Cutis Congenita – Plastic Reconstruction of three Scalp and Skull Defects with two Opposed Scalp Rotation Flaps and Split Thickness Skin Grafting
Publication History
received 26.05.2009
accepted 15.10.2009
Publication Date:
17 December 2009 (online)
Abstract
Aplasia cutis congenita (ACC) is a rare congenital defect of skin and subcutaneous tissue, more rarely of periosteum, skull and dura. The lesions can involve any location, but most common are scalp defects. We report on the successful treatment of three large defects of the scalp with skull involvement in a newborn girl by early debridement and defect closure with two opposed scalp rotation flaps and an occipital split-thickness skin graft.
Key words
aplasia cutis congenita (ACC) - congenital skull defects - scalp rotation flap
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Correspondence
Dr. Saskia M. Schnabl
Department of Plastic and Hand Surgery
University of Erlangen
Krankenhausstraße 12
91054 Erlangen
Germany
Phone: +49/9131/85 0
Fax: +49/9131/85 39327
Email: Saskia.Schnabl@uk-erlangen.de