Thorac Cardiovasc Surg 2010; 58(2): 76-80
DOI: 10.1055/s-0029-1186277
Original Cardiovascular

© Georg Thieme Verlag KG Stuttgart · New York

Valve-Sparing Operation for Aortic Root Aneurysm in Patients with Marfan Syndrome

R. Wang1 , W. G. Ma1 , L. X. Tian1 , L. Z. Sun1 , Q. Chang1
  • 1Department of Cardiovascular Surgery, Fu Wai Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China
Further Information

Publication History

received July 24, 2009

Publication Date:
23 March 2010 (online)

Abstract

Background: We report our experience with aortic valve-sparing procedures in patients with Marfan syndrome and aortic root aneurysm. Methods: Between August 2003 and July 2007, we performed aortic valve-sparing procedures in 20 patients with aortic root aneurysm resulting from Marfan syndrome. Mean age was 28 ± 10 years (range, 10 to 57 years), and there were 9 females and 11 males. A reimplantation technique was used in 9 cases, a remodeling technique in 8 and a patch technique in 3 cases. Additional procedures included total aorta replacement in 1 patient, and aortic arch replacement plus stented elephant trunk in 2 patients. The mean follow-up time was 46 ± 16 months (range, 17 to 64 months). Results: No in-hospital or late death occurred. Reexploration for bleeding was required in one case on postoperative day 1. No valve-related complications occurred during the follow-up period. At the end of follow-up, trivial or no aortic regurgitation was demonstrated in 14 patients, mild in 4 patients, moderate in 1 and severe in 1. Two patients with moderate and severe aortic regurgitation required reoperation. Conclusions: The early and mid-term results of the valve-sparing operations were favorable, and the durability of the preserved valve should encourage use of this technique in patients with Marfan syndrome.

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Dr. Lizhong Sun, MD

Department of Cardiovascular Surgery
Cardiovascular Institute and Fu Wai Hospital
Chinese Academy of Medical Sciences and Peking Union Medical College

167 Belishi Road

100037 Beijing

China

Phone: + 86 10 88 39 89 37

Fax: + 86 10 68 31 31 02

Email: slzh_2005@yahoo.com.cn