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CC BY-NC-ND 4.0 · AJP Rep 2024; 14(03): e202-e204
DOI: 10.1055/a-2385-1263
Case Report

A Case of Vein of Galen Aneurysmal Malformation Diagnosed Prenatally in a Monochorionic-Diamniotic Twin Pregnancy

Dana Senderoff Berger 
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Andre Robinson
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Judith Chervenak
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Kristen Thomas
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Ranjini Srinivasan
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Geeta Sharma
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Ashley S. Roman
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Christina A. Penfield
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
,
Meghana Limaye 
1   Department of Obstetrics and Gynecology, NYU Langone Medical Center, New York, New York
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Abstract

We present a case of a vein of Galen aneurysmal malformation (VGAM), a rare congenital arteriovenous malformation, in one fetus of a monochorionic-diamniotic twin pregnancy. The diagnosis was made with color Doppler ultrasonography at 28 weeks and the affected fetus was found to have worsening cardiomegaly on subsequent fetal echocardiograms. She was emergently delivered at 32 weeks for abnormal fetal heart rate tracing of the affected twin. Magnetic resonance imaging of the brain findings after delivery demonstrated severe neurological injury; therefore, postnatal embolization was not performed. The neonate died on day of life 9. The cotwin survived without neurological complications. This is the first case in the literature of a VGAM diagnosed prenatally in a monochorionic-diamniotic twin pregnancy and demonstrates the challenge of delivery timing with prenatal diagnosis in a twin pregnancy.

Keywords

twin anomaly - twin pregnancy - vein of Galen aneurysmal malformation


Publication History

Received: 08 July 2024

Accepted: 04 August 2024

Accepted Manuscript online:
13 August 2024

Article published online:
29 August 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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