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CC BY-NC-ND 4.0 · AJP Rep 2024; 14(01): e26-e30
DOI: 10.1055/a-2208-0032
Case Report

Case Series of Reproductive Outcomes after Surgical Correction of Obstructed Hemivagina in OHVIRA

Megan E. Bunnell 
1   Department of Obstetrics and Gynecology, Brigham and Women's Hospital, Boston, Massachusetts
,
Danielle T. Cipres 
2   Department of Pediatric and Adolescent Gynecology, Boston Children's Hospital, Boston, Massachusetts
,
Marc R. Laufer
2   Department of Pediatric and Adolescent Gynecology, Boston Children's Hospital, Boston, Massachusetts
› Author Affiliations Funding None.
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Abstract

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) is a rare congenital developmental syndrome manifested by uterine duplication, lower genital tract obstruction, and unilateral renal anomaly. Literature on reproductive outcomes in this patient population is limited. The aim of this study is to describe obstetric outcomes after surgical correction of obstructed hemivagina in a longitudinal cohort of patients with a diagnosis of OHVIRA. All cases of OHVIRA presenting to a single tertiary care children's hospital from 1990 to 2021 were retrospectively reviewed. Three cases demonstrating a variety of clinically important reproductive outcomes are described in detail including risks such as retained products, endometritis, preterm labor, and malpresentation. Understanding the reproductive outcomes associated with this diagnosis is important for practitioners seeking to counsel and care for patients with this diagnosis. This case series demonstrates a wide array of potential gynecologic and obstetric risks, though ultimately with successful term and near-term pregnancies.

Keywords

hemivagina - renal agenesis - infertility - Mullerian anomaly

Attestation

● Data regarding any of the subjects in the study has not been previously published unless specified.


● Data will be made available to the editors of the journal for review or query upon request.


Capsule

Reproductive outcomes after OHVIRA surgery are generally favorable but include a number of clinical risks that are important for patient–provider counseling.




Publication History

Received: 02 March 2023

Accepted: 19 October 2023

Accepted Manuscript online:
09 November 2023

Article published online:
23 January 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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